6080yyy午夜理论av片,黄片aaawww,国产色婷婷激情片,久久午夜国产精品,久久色av网址导航,销魂美女做爰免费视频,日韩黄色三级电影在线观看,在线电影人妻在线观看,日本高清成人片www网站免费,长途公共汽车上的轮杆

歡迎來到上海通蔚!

021-54845833/15800441009

品質(zhì)保證 · 通蔚試劑

當前位置: 首頁 > 科研產(chǎn)品 > 科研抗體 > 其他抗體 > CLCN7 抗原(重組蛋白)

產(chǎn)品中心

  • CLCN7 抗原(重組蛋白)

    規(guī)格:
    價格:
    • 品牌 : 通蔚生物
    • 目錄號 : TW16289
    • 應(yīng)用 : 僅限于科研使用
    • 保存條件 : 低溫保存
    • 貨期 : 現(xiàn)貨
    • 商品庫存:60
  • 商品詳情
  • 參考文獻
  • 說明書下載
  • 商品評論0
  • 相關(guān)產(chǎn)品

中文名稱: CLCN7 抗原(重組蛋白)

英文名稱: CLCN7 Antigen (Recombinant Protein)

別     名: chloride voltage-gated channel 7; CLC7; CLC-7; OPTA2; OPTB4; PPP1R63

儲     存: 冷凍(-20℃)

相關(guān)類別: 抗原

概    述

Fusion protein corresponding to a region derived from 606-805 amino acids of human CLCN7

技術(shù)規(guī)格

Full name:

chloride voltage-gated channel 7

Synonyms:

CLC7; CLC-7; OPTA2; OPTB4; PPP1R63

Swissprot:

P51798

Gene Accession:

BC012737

Purity:

>85%, as determined by Coomassie blue stained SDS-PAGE

Expression system:

Escherichia coli

Tags:

His tag C-Terminus, GST tag N-Terminus

Background:

The product of this gene belongs to the CLC chloride channel family of proteins. Chloride channels play important roles in the plasma membrane and in intracellular organelles. This gene encodes chloride channel 7. Defects in this gene are the cause of osteopetrosis autosomal recessive type 4 (OPTB4), also called infantile malignant osteopetrosis type 2 as well as the cause of autosomal dominant osteopetrosis type 2 (OPTA2), also called autosomal dominant Albers-Schonberg disease or marble disease autosoml dominant. Osteopetrosis is a rare genetic disease characterized by abnormally dense bone, due to defective resorption of immature bone. OPTA2 is the most common form of osteopetrosis, occurring in adolescence or adulthood.